Uterine perivascular epithelioid cell tumor (PEComa) in a pediatric patient: case report
DOI:
https://doi.org/10.35509/01239015.888Keywords:
Perivascular epithelioid cell neoplasms, uterine neoplasmsAbstract
PEComa is a perivascular epithelioid cell tumor of mesenchymal origin. These tumors correspond to a rare group of neoplasms. About 100 cases have been reported, of which only 30% are of gynecological origin, and the uterine body is the most frequent site. Due to its low frequency of appearance, there is no established medical conduct and treatment, which is why the management of this entity is a challenge. Presentation in the pediatric population is extremely rare, with limited data on its frequency in this age group. We present the case of a 13-year-old patient who consulted for pelvic pain. Diagnostic images were performed that documented a solid right para-adnexal mass. She was taken to surgery, which evidenced a tumor dependent on the uterine body with histology corresponding to a PEComa with characteristics of malignant behavior.
Author Biographies
Santiago Vieira-Serna, Fellow Unidad Funcional Ginecología, Instituto Nacional de Cancerología, Bogotá, D.C., Colombia.
1. Fellow Unidad Funcional Ginecología, Instituto Nacional de Cancerología, Bogotá, D.C., Colombia.
2. Posgrado de Ginecología Oncológica, Universidad Militar Nueva Granada, Bogotá, D.C., Colombia.
Claudia Rojas Salamanca, Servicio Ginecología Clínica de Marly Jorge Cavelier Gaviria, Bogotá, D.C., Colombia.
3. Servicio Ginecología Clínica de Marly Jorge Cavelier Gaviria, Bogotá, D.C., Colombia.
Diana Jimena Santana-Ballesteros, Departamento de Ginecología Oncológica, Clínica Colsanitas, Bogotá, D.C., Colombia.
4. Departamento de Ginecología Oncológica, Clínica Colsanitas, Bogotá, D.C., Colombia.
5. Unidad Funcional Ginecología, Instituto Nacional de Cancerología, Bogotá, D.C., Colombia.
Oscar Fernando Serrano-Ortiz, Departamento de Ginecología Oncológica, Clínica Colsanitas, Bogotá, D.C., Colombia.
4. Departamento de Ginecología Oncológica, Clínica Colsanitas, Bogotá, D.C., Colombia.
Lina María Caicedo-Páez, Departamento de Ginecología Oncológica, Clínica Colsanitas, Bogotá, D.C., Colombia.
4. Departamento de Ginecología Oncológica, Clínica Colsanitas, Bogotá, D.C., Colombia.
David Andrés Viveros-Carreño, Departamento de Ginecología Oncológica, Clínica Colsanitas, Bogotá, D.C., Colombia.
4. Departamento de Ginecología Oncológica, Clínica Colsanitas, Bogotá, D.C., Colombia.
5. Unidad Funcional Ginecología, Instituto Nacional de Cancerología, Bogotá, D.C., Colombia.
6. Departamento de Ginecología Oncológica, Clínica Los Nogales, Bogotá, D.C., Colombia.
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