Erdheim-Chester Disease: Pathological fracture of the left humerus
Keywords:
Erdheim-Chester, Fracture, Pathological, HistiocytosisAbstract
The Erdheim-Chester disease is a rare presentation of non-Langerhans cell histiocytosis. The etiology is unknown, and is more common in adults. The clinical manifestations are heterogeneous due to histiocytic infiltration of multiple systems. When there is skeletal involvement, it produces bone pain, and may be associated with interstitial, heart, liver, kidney or pulmonary infiltrates1-3. A case is presented on a patient who began with chronic bone pain and a pathological fracture of the left humerus with polyostotic involvement and with no evidence of multisystemic disease.
Author Biographies
Luis Gómez, Instituto Nacional de Cancerología
Grupo Ortopedia Oncológica, Instituto Nacional de Cancerología, Bogotá D.C., Colombia
Universidad Militar Nueva Granada, Bogotá D.C., Colombia
Camilo Soto, Instituto Nacional de Cancerología
Grupo Ortopedia Oncológica, Instituto Nacional de Cancerología, Bogotá D.C., Colombia
Universidad Militar Nueva Granada, Bogotá D.C., Colombia
Felipe Criollo, Instituto Nacional de Cancerología
Grupo Ortopedia Oncológica, Instituto Nacional de Cancerología, Bogotá D.C., Colombia
Universidad Militar Nueva Granada, Bogotá D.C., Colombia
Óscar Messa, Instituto Nacional de Cancerología
Grupo de Patología Oncológica, Instituto Nacional de Cancerología, Bogotá D.C., Colombia
Ricardo Romo, Fundación Universitaria San José
Posgrado de Ortopedia, Fundación Universitaria San José, Bogotá D.C., Colombia
Irene Patrón, Pontificia Universidad Javeriana
Posgrado de Ortopedia, Pontificia Universidad Javeriana, Bogotá D.C., Colombia
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