Giant congenital orbital teratoma: Case report

Authors

  • Luz Ángela Urcuqui Instituto Nacional de Cancerología
  • Daniel Ozaeta Instituto Nacional de Cancerología
  • Amaranto Suárez Instituto Nacional de Cancerología
  • Óscar Mesa Instituto Nacional de Cancerología
  • Francis Graziano Instituto Nacional de Cancerología
  • Mauricio Forero Instituto Nacional de Cancerología

Keywords:

Teratoma, Orbitat, Newborn

Abstract

The teratomas are tumors composed of tissues derived from all three germ layers which can be located in the gonads and extragonadal. The orbital location are rare and usually occur in healthy newborns producing proptosis. The authors present the case of a newborn with congenital orbital teratoma large invading intraocular structures and extending to the middle cranial fossa through the apex of the orbit. Clinical features, radiological findings, surgical approach, histopathologic description and adjuvant chemotherapy received by the patient are described.

Author Biographies

Luz Ángela Urcuqui, Instituto Nacional de Cancerología

Clínica de Hemato-oncología Pediátrica, Instituto Nacional de Cancerología, Bogotá D. C., Colombia

Posgrado Hemato-Oncología Pediátrica, Universidad Militar Nueva Granada, Bogotá D. C., Colombia

Daniel Ozaeta, Instituto Nacional de Cancerología

Clínica de Hemato-oncología Pediátrica, Instituto Nacional de Cancerología, Bogotá D. C., Colombia

Posgrado Hemato-Oncología Pediátrica, Universidad Militar Nueva Granada, Bogotá D. C., Colombia

Amaranto Suárez, Instituto Nacional de Cancerología

Clínica de Hemato-oncología Pediátrica, Instituto Nacional de Cancerología, Bogotá D. C., Colombia

Óscar Mesa, Instituto Nacional de Cancerología

Servicio de patología, Instituto Nacional de Cancerología, Bogotá D. C., Colombia

Francis Graziano, Instituto Nacional de Cancerología

Servicio de patología, Instituto Nacional de Cancerología, Bogotá D. C., Colombia

Mauricio Forero, Instituto Nacional de Cancerología

Servicio de imágenes diagnósticas, Instituto Nacional de Cancerología, Bogotá D. C., Colombia

References

Olson TA, Schneider DT, Perlman EJ. Germ cell tumors. En: Pizzo PA, Poplack DC, editores. Principles and Practices of Pediatric Oncology. 6 ed. Philadelphia: Lippinccott Williams and Wilkins; 2011. p. 1045-67.

Schneider DT, Olson TA. Germ Cell Tumors of the head and neck. En: Schneider DT, Brecht IB, Olson TA, Ferrari A, editores. Rare tumors in children and adolescents. Ed. Springer-Verlag Berlin Heidelberg; 2012. p. 169-73.

https://doi.org/10.1007/978-3-642-04197-6_19

Tapper D, Lack EE. Teratomas in infancy and childhood: A 54 year experience at the Children's Hospital Medical Center. Ann of Surg. 1983;198(3):398-409.

https://doi.org/10.1097/00000658-198309000-00016

Brodsky JR, Kanwar VS, Stafford LM, Reza R, Frazier L. Germ cell tumors/Teratoma. En: Reza Rahbar, Carlos Rodríguez-Galindo, John G, Maera, Edward R, Smith, Antonio R, Perez-Atayde, editores. Pediatric Head and Neck Tumors. Ed. Springer New York Heidelberg Dordrecht London; 2014. p. 153-63.

https://doi.org/10.1007/978-1-4614-8755-5_20

Sesenna E, Ferri A, Thai E, Magri AS. Huge orbital teratoma with intracranial extension: a case report. J Pediatr Surg. 2010;45(5):E27-31.

https://doi.org/10.1016/j.jpedsurg.2010.01.031

González C, Restrepo CA, Salazar GI, Monsalve P. Congenital orbital teratoma. Informe de caso Colomb Med. 2012;43: 82-5.

https://doi.org/10.25100/cm.v43i1.1062

Rattan KN, Malik V, Khurana P, Dhawan S, Kaushal V, Maggu S. Teratomas in infancy and childhood. Indian J Pediatr. 2001;68(2):117-20.

https://doi.org/10.1007/BF02722026

Dehner LP. Gonadal and extragonadal germ cell neoplasia of childhood. Hum Pathol. 1983;14(6):493-511.

https://doi.org/10.1016/S0046-8177(83)80004-5

Grube P, Hobart RI, Martínez MA, Gómez SM, Alderete G. Proptosis congénita secundaria a teratoma orbitario. Estudio clinicopatológico Arch Soc Esp Oftalmol. 2013;88(4):153-6.

https://doi.org/10.1016/j.oftal.2012.04.017

Schneider DT, Terenziani M, Cecchetto G, Olson TA. Gonadal and extragonadal germ cell tumors, sex cord stromal and rare gonadal tumors. En: Schneider, D.T., Brecht, I.B., Olson, T.A., Ferrari, A., editors. Rare tumors in children and adolescents. Ed. Springer-Verlag Berlin Heidelberg; 2012. 327-402.

https://doi.org/10.1007/978-3-642-04197-6_39

Mee JJ, McKelvie PA, McNab AA. Orbital teratoma: late presentation with normal vision. Clin Experiment Ophthalmol. 2002;30:41-3.

https://doi.org/10.1046/j.1442-9071.2002.00479.x

Frazier AL, Amatruda JF. Pediatric germ cell tumors. En: Orkin S, Fisher D, Look AT, Lux S, Ginsburg D, Nathan DG, editores. Oncology of infancy and childhood. Ed. Philadelphia: Saunders Elsevieer; 2009. p. 911-61.

https://doi.org/10.1016/B978-1-4160-3431-5.00023-6

Herman TE, Vachharajani A, Siegel MJ. Massive congenital orbital teratoma. J Perinatol. 2009;29(5):396-7.

https://doi.org/10.1038/jp.2008.205

Göbel U, Calaminus G, Engert J, Kaatsch P, Gadner H, Bökkerink JP, et al. Teratomas in infancy and childhood. Med Pediatr Oncol. 1998;3(1):8-15.

https://doi.org/10.1002/(SICI)1096-911X(199807)31:1<8::AID-MPO2>3.0.CO;2-H

Marina NM, Cushing B, Giller R, Cohen L, Lauer SJ, Ablin A, et al. Complete surgical excision is effective treatment for children with immature teratomas with or without malignant elements: A Pediatric Oncology Group/Children's Cancer Group Intergroup Study. J Clin Oncol. 1999;17(7):2137-43.

https://doi.org/10.1200/JCO.1999.17.7.2137

How to Cite

[1]
Urcuqui, L.A. et al. 2015. Giant congenital orbital teratoma: Case report. Revista Colombiana de Cancerología. 19, 1 (Mar. 2015), 53–58.

Downloads

Download data is not yet available.

Published

2015-03-01

Issue

Section

Reportes de caso