Ectopic Cushing Syndrome: A literature review
Keywords:
Cushing’s syndrome, Neuroendocrine Tumors, Carcinoids, ACTH syndrome ectopic, Paraneoplastic endocrine syndromeAbstract
Cushing’s syndrome is a very rare disease associated with significant morbidity and mortality. It is classified as adrenocorticotropic hormone (ACTH) dependent (Pituitary and ectopic tumors) or ACTH independent (lesions of adrenal origin). In most cases, pituitary tumors are responsible for the Cushing‘s syndrome, followed by adrenal lesions and finally by ectopic tumors (5-15% of all cases). This article describes the most important epidemiological, clinical, diagnostic and therapeutic aspects of ectopic tumors causing Cushing’s syndrome.
Author Biographies
Johnayro Gutiérrez-Restrepo, Hospital Pablo Tobón Uribe
Servicio de Medicina Interna, Hospital Pablo Tobón Uribe, Servicio de Endocrinología y Metabolismo, Universidad de Antioquia, Medellín, Colombia
Alejandro Román-González, Hospital Universitario San Vicente Fundación
Unidad de Medicina Interna, Hospital Universitario San Vicente Fundación, Medellín, Colombia
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