Tumor desmoplásico de célula pequeña y redonda paratesticular/testicular: reporte de caso y revisión de la literatura.

Autores/as

  • Handerson Rafael Osma Charris Instituto Nacional de Cancerología
  • Fernando Contreras Mejía Instituto Nacional de Cancerología
  • Camilo Vallejo Yepes Instituto Nacional de Cancerología
  • Carolina Bautista Saiz Fundación Universitaria Ciencias de la Salud (FUCS).
  • Vilma Medina Boada Instituto Nacional de Cancerología
  • Tatiana Roncancio Velandia Instituto Nacional de Cancerología

DOI:

https://doi.org/10.35509/01239015.691

Palabras clave:

Tumor Desmoplásico de Células Pequeñas Redondas; Sarcoma; Sarcoma de Células Pequeñas; Sarcoma de Ewing; Quimioterapia.

Resumen

El tumor desmoplásico de célula redonda y pequeña (TDCRP) es una patología neoplásica maligna agresiva y poco común. Afecta predominantemente a hombres entre la segunda y tercera década de la vida. Los pacientes que la padecen tienen un pobre pronóstico, con una supervivencia global a 5 años de hasta el 30%. Se presenta generalmente como una masa en la cavidad abdominal, frecuentemente multifocal. Para su tratamiento se recomienda un enfoque multimodal, con cirugía, quimioterapia y radioterapia. Poco más de 20 casos de TDCRP a nivel testicular/paratesticular se han reportado en la literatura. A continuación, presentamos un caso ilustrativo en ésta localización, se discute el caso y se realiza revisión de la literatura.

Biografía del autor/a

Handerson Rafael Osma Charris, Instituto Nacional de Cancerología

Fellow Oncología Clínica.

Fernando Contreras Mejía, Instituto Nacional de Cancerología

Oncólogo Clínico.

Camilo Vallejo Yepes, Instituto Nacional de Cancerología

Fellow Oncología Clínica. 

 

Carolina Bautista Saiz, Fundación Universitaria Ciencias de la Salud (FUCS).

Residente de Patología.

Vilma Medina Boada, Instituto Nacional de Cancerología

Departamento de Genética y Oncología molecular.

Tatiana Roncancio Velandia, Instituto Nacional de Cancerología

Departamento de Genética y Oncología molecular.

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Cómo citar

[1]
Osma Charris, H.R. et al. 2020. Tumor desmoplásico de célula pequeña y redonda paratesticular/testicular: reporte de caso y revisión de la literatura . Revista Colombiana de Cancerología. 24, 3 (jul. 2020), 125–134. DOI:https://doi.org/10.35509/01239015.691.

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03-07-2020

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