Malformación arteriovenosa asociada enmascara un ganglioglioma anaplásico multifocal en un adolescente

  • Gustavo Adolfo Carvajal-Barrios Universidad el Bosque
  • Jimena Ortiz Hospital Militar Central
  • Natalia González Hospital Militar Central
  • José Arias Hospital Militar Central
  • Fernando Velandia Universidad del Rosario
  • Pilar Guerrero Hospital Militar Central
  • Eugenia Espinosa Hospital Militar Central
Palabras clave: Tumor cerebral, Niño, Hipertensión endocraneana, Ganglioglioma, Cefalea

Resumen

El ganglioglioma anaplásico grado III es un tumor del sistema nervioso central (SNC) agresivo, infrecuente y radiosensible. Afecta más a hombres en una relación 1,3 a 1. Su pico de incidencia se encuentra en la tercera década de la vida. Existen solo 10 casos registrados en niños en Colombia desde el 2000 al 2014, con desenlace fatal a pesar de la radioterapia. Se presenta un caso de un adolescente que debutó con cefalea con signos de alarma asociado a una malformación arteriovenosa que dificultó el diagnóstico de este raro tumor, cuya presentación fue la más agresiva: la forma multicéntrica. El conocer las manifestaciones clínicas de lesiones intracraneales ocupantes de espacio facilita la evaluación y tratamiento a los niños afectados.

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Biografía del autor/a

Gustavo Adolfo Carvajal-Barrios, Universidad el Bosque

Physician, pediatrics resident, Universidad el Bosque, Bogotá D. C, Colombia

Jimena Ortiz, Hospital Militar Central

Neuroradiologist, professor ad honorem, Universidad Militar Nueva Granada (UMNG)-Hospital Militar Central (HMC), Bogotá D.C, Colombia

Natalia González, Hospital Militar Central

Pediatric hematologist/oncologist, HMC-HMC, Bogotá D. C, Colombia

José Arias, Hospital Militar Central

Pathologist, HMC. Professor ad honorem UMNG-HMC, Bogotá D. C, Colombia

Fernando Velandia, Universidad del Rosario

Neuropathologist, Senior professor, Neuroscience Group, Universidad del Rosario, Bogotá D. C, Colombia

Pilar Guerrero, Hospital Militar Central

Pediatric neurologist, associate professor of pediatric neurology, UMNG-HMC, Bogotá D. C, Colombia

Eugenia Espinosa, Hospital Militar Central

Pediatric neurologist, tenured profesor in pediatric neurology UMNG-HMC, Coordinator of graduate studies in pediatric
neurology UMNG-HMC, Bogotá D. C, Colombia

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Publicado
2018-12-01
Cómo citar
[1]
Carvajal-Barrios, G.A., Ortiz, J., González, N., Arias, J., Velandia, F., Guerrero, P. y Espinosa, E. 2018. Malformación arteriovenosa asociada enmascara un ganglioglioma anaplásico multifocal en un adolescente. Revista Colombiana de Cancerología. 22, 4 (dic. 2018), 180-185.
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